Fulminant Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis.

نویسندگان

  • Silvia Bohne
  • Karim Kentouche
  • Iver Petersen
  • Michael Fritzenwanger
  • Mathias W Pletz
  • Kai Lehmberg
  • Paul La Rosée
  • Orlando Guntinas-Lichius
چکیده

Hemophagocytic lymphohistiocytosis (HLH) is a rare, severe, and often fatal disorder. Its hereditary and sporadic form can present as a significant diagnostic challenge to the otolaryngologist. This report describes two fatal cases of adult patients with HLH initially presented as infectious mononucleosis to an otorhinolaryngologist. The clinical presentation, serological and histological features, and management are discussed.

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عنوان ژورنال:
  • The Laryngoscope

دوره 123 2  شماره 

صفحات  -

تاریخ انتشار 2013